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Fatal insomnia

From Wikipedia
fatal familial insomnia
class of disease, signs den symptoms
Short nameFFI Edit
Health specialtypsychiatry, sleep medicine, neuropathology Edit
Genetic associationPRNP Edit
ICD-9-CM046.72 Edit
ICPC 2 IDN73 Edit
NCI Thesaurus IDC84711 Edit

Fatal insomnia be a neurodegenerative disease wey dey result in trouble sleeping as ein hallmark symptom.[1] De majority of cases be familial (fatal familial insomnia [FFI]), wey dey stem from a mutation insyd de PRNP gene, plus de remainder of cases wey dey occur sporadically (sporadic fatal insomnia [sFI]). De problems plus sleeping typically dey start out gradually den worsen over time.[2] Eventually, de patient go succumb to total insomnia (agrypnia excitata), most often wey dey lead to oda symptoms such as speech problems, coordination problems, den dementia.[3] E dey result in death within a few months to a few years, wey der no be known disease-modifying treatment.[1]

References

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  1. 1 2 "Fatal Insomnia - Neurologic Disorders". Merck Manual Professional Edition (in Canadian English). Retrieved 2026-01-15.
  2. "Fatal Familial Insomnia Symptoms, Causes, Treatment | NORD" (in American English). Retrieved 2026-01-15.
  3. "Fatal Insomnia". Merck Manual. Retrieved 4 May 2018.
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